The European sarcoma guideline sets out referral to reference centres, biopsy and molecular diagnosis, surgery with radiotherapy for localised disease, the selective use of chemotherapy, and histology-driven treatment of advanced disease.
Joint European guideline covering the diagnosis, staging, multidisciplinary management and follow-up of soft tissue and visceral sarcomas in adults, including limb and trunk sarcomas, retroperitoneal sarcoma, gastrointestinal stromal tumour, desmoid tumours and subtype-specific systemic therapy recommendations.
The general principles on the sarcoma subtype pages (reference centre surgery, radiotherapy for high-grade deep tumours, doxorubicin first line, histology-directed later lines) follow this guideline.
Shares Myxofibrosarcoma, Malignant peripheral nerve sheath tumour (MPNST), Undifferentiated pleomorphic sarcoma (UPS), Leiomyosarcoma.
Shares Myxofibrosarcoma, Retroperitoneal sarcoma, Undifferentiated pleomorphic sarcoma (UPS), Soft tissue sarcoma of the extremity (localised and advanced).
Shares Retroperitoneal sarcoma, Liposarcoma, Undifferentiated pleomorphic sarcoma (UPS), Leiomyosarcoma.
Shares Robin L. Jones, Annals of Oncology.
Shares Retroperitoneal sarcoma, Leiomyosarcoma, Soft tissue sarcoma of the extremity (localised and advanced).
Shares Retroperitoneal sarcoma, Liposarcoma, Leiomyosarcoma.
Shares Malignant peripheral nerve sheath tumour (MPNST), Undifferentiated pleomorphic sarcoma (UPS), Soft tissue sarcoma of the extremity (localised and advanced).
Shares Myxofibrosarcoma, Perivascular epithelioid cell tumour (PEComa), Malignant peripheral nerve sheath tumour (MPNST), Undifferentiated pleomorphic sarcoma (UPS).